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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">pirogovestnik</journal-id><journal-title-group><journal-title xml:lang="ru">Вестник Национального медико-хирургического центра им. Н.И. Пирогова</journal-title><trans-title-group xml:lang="en"><trans-title>Bulletin of Pirogov National Medical &amp; Surgical Center</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">2072-8255</issn><issn pub-type="epub">2782-3628</issn><publisher><publisher-name>Национальный медико-хирургический Центр им. Н.И. Пирогова</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.25881/20728255_2026_21_3_172</article-id><article-id custom-type="elpub" pub-id-type="custom">pirogovestnik-673</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>КЛИНИЧЕСКИЕ НАБЛЮДЕНИЯ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>CASE REPORTS</subject></subj-group></article-categories><title-group><article-title>ХИРУРГИЧЕСКОЕ ЛЕЧЕНИЕ ПАЦИЕНТА С ОСТРЫМ РАССЛОЕНИЕМ АОРТЫ I ТИПА, ОСЛОЖНЕННОГО ЦЕРЕБРАЛЬНОЙ МАЛЬПЕРФУЗИЕЙ С ПРИМЕНЕНИЕМ АДАПТИВНОЙ ПЕРФУЗИИ И ТЕХНИКИ «BRANCH-FIRST»</article-title><trans-title-group xml:lang="en"><trans-title>SURGICAL TREATMENT OF A PATIENT WITH ACUTE TYPE A AORTIC DISSECTION COMPLICATED BY CEREBRAL MALPERFUSION USING ADAPTIVE PERFUSION AND THE BRANCH-FIRST TECHNIQUE</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Мироненко</surname><given-names>В. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Mironenko</surname><given-names>V. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Москва</p></bio><bio xml:lang="en"><p>Moscow</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Гарманов</surname><given-names>С. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Garmanov</surname><given-names>S. V.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Москва</p></bio><bio xml:lang="en"><p>Moscow</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Мамилов</surname><given-names>М-Б. Т.</given-names></name><name name-style="western" xml:lang="en"><surname>Mamilov</surname><given-names>M-B. T.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Москва</p></bio><bio xml:lang="en"><p>Moscow</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Дарвиш</surname><given-names>Н. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Darvish</surname><given-names>N. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Москва</p></bio><bio xml:lang="en"><p>Moscow</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Исмаилов</surname><given-names>С. С.</given-names></name><name name-style="western" xml:lang="en"><surname>Ismailov</surname><given-names>S. S.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Москва</p></bio><bio xml:lang="en"><p>Moscow</p></bio><email xlink:type="simple">isaidazim@bk.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Федоров</surname><given-names>Н. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Fedorov</surname><given-names>N. V.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Москва</p></bio><bio xml:lang="en"><p>Moscow</p></bio><xref ref-type="aff" rid="aff-1"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>ФГБУ «Национальный медицинский исследовательский центр сердечно-сосудистой  хирургии им. А.Н. Бакулева»</institution><country>Россия</country></aff><aff xml:lang="en"><institution>Bakoulev National Medical Research Center for Cardiovascular Surgery</institution><country>Russian Federation</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2026</year></pub-date><pub-date pub-type="epub"><day>03</day><month>09</month><year>2026</year></pub-date><volume>21</volume><issue>3</issue><fpage>172</fpage><lpage>176</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Мироненко В.А., Гарманов С.В., Мамилов М.Т., Дарвиш Н.А., Исмаилов С.С., Федоров Н.В., 2026</copyright-statement><copyright-year>2026</copyright-year><copyright-holder xml:lang="ru">Мироненко В.А., Гарманов С.В., Мамилов М.Т., Дарвиш Н.А., Исмаилов С.С., Федоров Н.В.</copyright-holder><copyright-holder xml:lang="en">Mironenko V.A., Garmanov S.V., Mamilov M.T., Darvish N.A., Ismailov S.S., Fedorov N.V.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://submit.pirogov-vestnik.ru/jour/article/view/673">https://submit.pirogov-vestnik.ru/jour/article/view/673</self-uri><abstract><p>Представлено клиническое наблюдение хирургического лечения пациента 50 лет с острым расслоением аорты I типа, осложненным выраженной церебральной мальперфузией и распространением расслоения на брахиоцефальные артерии. По данным МСКТ выявлены расслоение брахиоцефального ствола с тромбозом ложного просвета, стеноз правой общей сонной артерии, критический стеноз и тромбоз ложного просвета левой общей сонной артерии, а также поражение левой подключичной артерии. В связи с высоким риском периоперационной ишемии головного мозга, операция заключалась в первоочередном протезировании брахиоцефальных артерий по принципу «branch-first» с использованием трифуркационного протеза, после восстановления контролируемой церебральной перфузии проведены протезирование восходящей аорты и дуги аорты в условиях адаптивной перфузии головного мозга. Длительность искусственного кровообращения составила 232 мин, пережатия аорты – 101 мин, циркуляторного ареста – 36 мин. Послеоперационный период осложнился дыхательной и почечной недостаточностью, потребовавшей гемодиализа. Пациент выписан на 30-е сутки в удовлетворительном состоянии. Наблюдение демонстрирует клиническую реализуемость стратегии ранней церебральной реперфузии у больных с острым расслоением аорты I типа и тяжелым поражением брахиоцефальных артерий.</p></abstract><trans-abstract xml:lang="en"><p>A clinical case of surgical treatment of a 50-year-old patient with acute type A aortic dissection complicated by severe cerebral malperfusion and extension of the dissection into the brachiocephalic arteries is presented. Multislice CT revealed dissection of the brachiocephalic trunk with false lumen thrombosis, stenosis of the right common carotid artery, critical stenosis and false lumen thrombosis of the left common carotid artery, as well as involvement of the left subclavian artery. Given the high risk of perioperative cerebral ischemia, the operation was initiated with branch-first reconstruction of the brachiocephalic arteries using a trifurcated graft. After restoration of controlled cerebral perfusion, replacement of the ascending aorta and aortic arch was performed under adaptive cerebral perfusion. Cardiopulmonary bypass time – 232 min, cross-clamp – 101 min, and circulatory arrest – 36 min. The postoperative course was complicated by respiratory and renal failure requiring hemodialysis. The patient was discharged on postoperative day 30 in satisfactory condition.</p></trans-abstract><kwd-group xml:lang="ru"><kwd>острое расслоение аорты I типа</kwd><kwd>церебральная мальперфузия</kwd><kwd>branch-first</kwd><kwd>адаптивная перфузия головного мозга</kwd><kwd>брахиоцефальные артерии</kwd><kwd>хирургия дуги аорты</kwd></kwd-group><kwd-group xml:lang="en"><kwd>аcute type A aortic dissection</kwd><kwd>cerebral malperfusion</kwd><kwd>branchfirst</kwd><kwd>adaptive cerebral perfusion</kwd><kwd>brachiocephalic arteries</kwd><kwd>aortic arch surgery</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Sun J, Xue C, Zhang J, et al. Extra-anatomic revascularization and a new cannulation strategy for preoperative cerebral malperfusion due to severe stenosis or occlusion of supra-aortic branch vessels in acute type A aortic dissection. 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